Idiopathic Pulmonary Arterial Hypertension

(PPH; Unexplained Pulmonary Hypertension; Idiopathic Pulmonary Hypertension; Pulmonary Arterial Hypertension; Sporadic Primary Pulmonary Hypertension; Familial Primary Pulmonary Hypertension; Primary Pulmonary Hypertension)


Primary pulmonary hypertension (PPH) is a rare disease. It is high blood pressure in the blood vessels of the lungs.A person with PPH has extra muscle in the walls of these blood vessels. That extra muscle makes it more difficult for blood to flow through them. As a result, the right side of the heart has to work harder to push blood to the lungs. This additional strain can eventually lead to heart failure.PPH is a serious condition. It requires care from your doctor.
Heart and Lungs
BN00039 96472 1 sides labeled
Copyright © Nucleus Medical Media, Inc.


The cause of PPH is unknown. Several factors may contribute to the development of the disease, including:
  • Autoimmune diseases
  • Exposure to certain drugs or chemicals
  • Genetic defects

Risk Factors

PPH is more common in women aged 30-40 years. Other factors that may increase your risk of PPH include:
  • Liver cirrhosis
  • Portal hypertension
  • HIV infection
  • Family history of PPH
  • Use of appetite suppressants (diet pills)
  • Cocaine use


Initial symptoms of PPH may be minor. They will get progressively worse. PPH may cause:
  • Shortness of breath (when you are active or at rest)
  • Abnormally rapid, deep breathing—hyperventilation
  • Fatigue
  • Progressive weakness
  • Fainting spells
  • Lightheadedness
  • Coughing up blood
  • Bluish tint to the lips and skin—cyanosis
  • Swelling of the legs and hands
  • Chest pain
  • Lack of appetite
  • Cold hands and feet
  • Low blood pressure

leave comments
Did you like this? Share with your family and friends.
Related Topics:
Current Research From Top Journals

Music May Improve Sleep Quality in Adults with Insomnia
October 2015

Insomnia can make your days miserable and a cure can be hard to find. There are some medications but there is some worry with side effects and the potential for addiction. Music is side effect free and according to this study may help you find sleep.

dot separator
previous editions

CPAP May Help Older Adults with Obstructive Sleep Apnea
September 2015

Water Before Meals May Promote Weight Loss
August 2015

Fecal Transplants Induce Ulcerative Colitis Remission
July 2015

dashed separator


Our Free Newsletter
click here to see all of our uplifting newsletters »